Dernières publications

Chiffres clés

54 Publications avec texte intégral

Open Access

76 %

Mots clés

BMD Cardiomyopathy Knockout Human Umbilical Vein Endothelial Cells Calcium Channels Duchenne DMD dystrophy Cell Biology Modificateurs de gènes Clinical trials Isoforms Gene modifiers Activin Receptors Exon skipping DMO Inhibitors Adult muscle stem cells Delivery Dilated Cardiomyopathy CaVβ1 Cachexia Becker Muscular Dystrophy LncARN Mitochondrial fission Multiresolution modeling Mdx mouse Humans Becker muscular dystrophy BMD MiARN Inbred mdx DMD Dystrophie Musculaire de Duchenne DMD CTNNB1 Epigenetics Dystrophin Cultured Becker muscular dystrophy BMD Duchenne muscular dystrophy DMD miRNA nNOS Long noncoding RNA Mice Inbred C57BL Cell homeostasis Connexins Cell Line Molecular docking Muscle L-Type Base Sequence Antisense oligonucleotides Gene Expression Regulation/drug effects Dystrophin central domain Muscle Biology MES Hepatocellular carcinoma Calcium CaV subunits Genomic Hear Becker BMD muscular dystrophy Heart Failure Dystrophy Diseases Energy Metabolism/drug effects Génomique Liver Multi resolution modeling Dystrophine Metabolism CaVβs Long QT Immunoglobulin Fc Fragments/pharmacology Molecular Sequence Data Dystrophie Musculaire de Becker BMD Male Autophagy Morphogenesis Dystrophie musculaire de Becker Homeostasis Dystrophin-EGFP Jonction neuromusculaire JNM Duchenne muscular dystrophy DMD Animals Centronuclear myopathy Invivo DHPR α1S Dynamin 2 Multi exon skipping Becker muscular dystrophy Skeletal muscle Gene expression Ex-vivo Cardiomyopathie Dystrophie myotonique de type 1 DM1 CD38 Isoformes LncRNA LKB1 Drp1 Allele‐specific silencing therapy Cells Animal/physiopathology Duchenne muscular dystrophy